HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Hawkins, J. A. Articles by McGough, E. C. Search for Related Content PubMed PubMed Citation Articles by Hawkins, J. A. Articles by McGough, E. C.

The Journal of Thoracic and Cardiovascular Surgery, Vol 100, 492-497, Copyright © 1990 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association

ARTICLES

Early and late results in pulmonary atresia and intact ventricular septum

JA Hawkins, JK Thorne, MM Boucek, GS Orsmond, HD Ruttenberg, LG Veasy and EC McGough
Department of Surgery, University of Utah Medical Center, Salt Lake City.

We examined the early and late results of operations in 29 consecutive neonates with pulmonary atresia and intact ventricular septum treated from 1980 to 1988. Transventricular pulmonary valvotomy and central aorta-pulmonary artery shunting were performed in 19 of 22 infants who had a patent infundibulum. Pulmonary valvotomy alone was performed in 3 of the 22 infants with a patent infundibulum, but 2 of these required subsequent systemic-pulmonary artery shunts. Primary shunting was used to palliate 7 infants who had absent infundibular portions of the right ventricle and a very diminutive right ventricular cavity. Tricuspid valve excision and atrial septectomy were also performed in 5 of these 7 infants to decompress large fistulous communications between the right ventricule and coronary artery. Two early deaths (2/29, 6.9%) occurred overall. Both were in infants who had a very small right ventricle. Definitive operation has been accomplished in 16 patients; 13 have had closure of residual interatrial communications and shunt ligation with no deaths, and 3 have undergone modified Fontan repair with 1 death. Actuarial survival rate for the entire group, including operative deaths, is 86% at 5 years. The technique of transventricular pulmonary valvotomy and systemic-pulmonary artery shunting offers a reliable means of palliating neonates with pulmonary atresia and intact ventricular septum and obtains good late right ventricular growth. Systemic-pulmonary shunting, tricuspid valvectomy, and atrial septectomy may offer a means of reducing or obliterating right ventricular-coronary artery fistulas.

This article has been cited by other articles:

				K. J. Guleserian, L. B. Armsby, R. R. Thiagarajan, P. J. del Nido, and J. E. Mayer Jr Natural History of Pulmonary Atresia With Intact Ventricular Septum and Right-Ventricle-Dependent Coronary Circulation Managed by the Single-Ventricle Approach Ann. Thorac. Surg., June 1, 2006; 81(6): 2250 - 2258. [Abstract] [Full Text] [PDF]

				Y P Mi, A K T Chau, C S W Chiu, T C Yung, K S Lun, and Y F Cheung Evolution of the management approach for pulmonary atresia with intact ventricular septum Heart, May 1, 2005; 91(5): 657 - 663. [Abstract] [Full Text] [PDF]

				Y. Tanoue, H. Kado, T. Maeda, Y. Shiokawa, N. Fusazaki, and S. Ishikawa Left ventricular performance of pulmonary atresia with intact ventricular septum after right heart bypass surgery J. Thorac. Cardiovasc. Surg., November 1, 2004; 128(5): 710 - 717. [Abstract] [Full Text] [PDF]

				D. A. Ashburn, E. H. Blackstone, W. J. Wells, R. A. Jonas, F. A. Pigula, P. B. Manning, G. K. Lofland, W. G. Williams, B. W. McCrindle, and Members of the Congenital Heart Surgeons Society Determinants of mortality and type of repair in neonates with pulmonary atresia and intact ventricular septum J. Thorac. Cardiovasc. Surg., April 1, 2004; 127(4): 1000 - 1008. [Abstract] [Full Text] [PDF]

				N. Yoshimura, M. Yamaguchi, H. Ohashi, Y. Oshima, S. Oka, M. Yoshida, H. Murakami, and T. Tei Pulmonary atresia with intact ventricular septum: Strategy based on right ventricular morphology J. Thorac. Cardiovasc. Surg., November 1, 2003; 126(5): 1417 - 1426. [Abstract] [Full Text] [PDF]

				M. Alwi, K. Geetha, A. A. Bilkis, M. K. Lim, S. Hasri, A. L. Haifa, A. Sallehudin, and R. Zambahari Pulmonary atresia with intact ventricular septum percutaneous radiofrequency-assisted valvotomy and balloon dilation versus surgical valvotomy and blalock taussig shunt J. Am. Coll. Cardiol., February 1, 2000; 35(2): 468 - 476. [Abstract] [Full Text] [PDF]

				H. K. Najm, W. G. Williams, J. G. Coles, I. M. Rebeyka, and R. M. Freedom Pulmonary Atresia With Intact Ventricular Septum: Results of the Fontan Procedure Ann. Thorac. Surg., March 1, 1997; 63(3): 669 - 675. [Abstract] [Full Text]

				J. D. Waldman, R. B. Karp, J. J. Lamberti, M. E. Sand, D. G. Ruschhaupt, and B. Agarwala Tricuspid Valve Closure in Pulmonary Atresia and Important RV-to-Coronary Artery Connections Ann. Thorac. Surg., April 1, 1995; 59(4): 933 - 940. [Abstract] [Full Text]

				H. Laks, R. N. Gates, P. W. Grant, S. Drant, V. Allada, and B. Harake Aortic to Right Ventricular Shunt for Pulmonary Atresia and Intact Ventricular Septum Ann. Thorac. Surg., February 1, 1995; 59(2): 342 - 347. [Abstract] [Full Text]