The Journal of Thoracic and Cardiovascular Surgery, Vol 69, 361-364, Copyright © 1975 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association
Total sequestration of the right lung
JZ Jona and JG Raffensperger
A 2-day-old baby with severe respiratory distress and cyanosis was admitted
to the hospital with a totally opacified right pleural cavity. Preoperative
studies demonstrated absence of the right pulmonary artery, and a patent
ductus arteriosus, and a left pulmonary artery pressure of 85/45 mm. Hg.
The hypoplastic right lung received its entire blood supply from multiple
vessels through the diaphragm. The infant's condition improved initially
after a right pneumonectomy, but she died of progressive respiratory
insufficiency at the age of 7 months.