The Journal of Thoracic and Cardiovascular Surgery, Vol 69, 790-792, Copyright © 1975 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association
Radical surgical treatment of esophageal stenosis due to epidermolysis bullosa
J Kralik and V Rapant
Stenotic lesions of the esophagus in epidermolysis bullosa are a rare cause
of dysphagia. Even though 50 cases have been reported in the literature,
only recently has surgical treatment been suggested for these patients. In
our patients, who had an annular stenosis just distal to the
pharyngoesophageal juncture, resection of a mucosal cylindrical segment
with reanastomosis through a longitudinal esophageal myotomy was
successful. This method of treatment is suggested for patients in whom the
stenosis is localized.