The Journal of Thoracic and Cardiovascular Surgery, Vol 74, 70-72, Copyright © 1977 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association
Double-outlet right ventricle (S,D,D), VSD related to pulmonary artery, and pulmonic stenosis absent. Correction with an intraventricular conduit in infancy
S Stewart
The case history of a 5-month-old infant with double-outlet right ventricle
(S,D,D) ventricular septal defect (VSD) related to the pulmonary artery,
and absence of pulmonic stenosis is reported. The anomaly was repaired with
an internal intraventricular conduit. This is the youngest infant with this
subset of DORV to survive complete repair and the youngest in whom an
intraventricular conduit was used. The diagnosis was not suspected
preoperatively, and it is fortunate that the intracardiac anatomy permitted
this type of repair at this age. The optimal management program for this
subset of DORV should be initial pulmonary artery banding with later
complete repair.