The Journal of Thoracic and Cardiovascular Surgery, Vol 76, 710-717, Copyright © 1978 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association
Successful repair of double-outlet right ventricle, complete atrioventricular canal, and atrioventricular discordance associated with dextrocardia and pulmonary stenosis
GK Danielson, IF Tabry, DG Ritter and JD Maloney
The association of complete atrioventricular canal with other complex
congenital cardiac anomalies has represented a significant challenge for
the cardiac surgion. The combination of double-outlet right ventricle with
complete atrioventricular canal has been particularly difficult to correct,
with no surgical successes having been reported until recently. This is a
report of the first successful repair of double-outlet right ventricle,
complete atrioventricular canal, and atrioventricular discordance
(ventricular incersion) associated with common atrium, bilateral superior
venae cavae, dextrocardia, and pulmonary stenosis. The specialized
conduction tissue was identified by intracardiac electrophysiological
mapping, and normal sinus rhythm was preserved. Postoperative cardiac
catheterization showed excellent hemodynamics. One year postoperatively,
the patient was attending school, playing swimming without difficulty, and
taking no cardiac medications. This good result lends encouragement for
considering total repair for similar patients with the combination of
double-outlet right ventricle, complete atrioventricular canal, and other
associated congenital cardiac anomalies.