The Journal of Thoracic and Cardiovascular Surgery, Vol 92, 142-145, Copyright © 1986 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association
Coronary sinus septal defect associated with tricuspid atresia
JD Rumisek, JD Pigott, PM Weinberg and WI Norwood
Coronary sinus septal defects are unusual congenital anomalies that may
assume particular clinical importance in patients undergoing a modified
Fontan procedure. Two of 10 patients with tricuspid atresia who underwent a
modified Fontan procedure between January, 1984, and December, 1984, were
noted to have coronary sinus septal defects in the early postoperative
period. A pathologic review of 159 specimens of tricuspid atresia revealed
coronary sinus septal defects in four. Although infrequent, coronary sinus
septal defects may permit significant persistent right-to-left interatrial
shunting after a modified Fontan procedure. Ideally, preoperative
recognition allows for selective direct closure or closure of the coronary
sinus orifice. Alternatively, routine baffling of the coronary sinus into
the left atrium obviates this potential source of interatrial
communication.